We report an uncommon case of schwannoma of the hypoglossal nerve in a 39yearold woman presented. Malignant lesions of the skull base and nasopharynx are more frequent causes. Examination showed decreased right palate elevation and atrophy of right sternocleidomastoid, trapezius, and tongue with rightward tongue deviation, indicating collet sicard syndrome involving cranial nerves ixxii in jugular foramen and hypoglossal canal. The vernet, collet sicard and villaret syndromes are uncommon. He was receiving chemotherapy for appendiceal adenocarcinoma. The etiology is variable, including benign or malignant tumors, metastasis, infections, or idiopathic causes. Collet sicard syndrome may be diagnosed based on clinical history, a physical examination or imaging studies such as computed tomography ct and mri scans. Although this syndrome has been reported previously in the literature, most cases are diagnosed as part of primary disease followup. Examination was remarkable for left tongue atrophy and fibrillations, tongue deviation to the left, left vocal cord paralysis, and trapezius and sternocleidomastoid muscle wasting figure collet sicard syndrome, cn ixcnxii paralysis1,2. As tres sindromes podem ter diversas etiologias tais como.
Colletsicard syndrome as an initial presentation of. Collet sicard is a rare syndrome that involves paralysis of unilateral lower cranial nerves ix, x, xi and xii due to lesions at the base of the skull. Background collet sicard syndrome is caused by lesions at the base of the skull affecting the lower cranial nerves. This case is unusual because of the diagnosis of bone metastasis secondary to.
Collet sicard syndrome is a very rare condition characterised by unilateral palsy of the ixxii cranial nerves. Colletsicard syndrome is an uncommon clinical manifestation of skull base disease involving the jugular and hypoglossal foramina, with consequent palsies of cranial nerves ix, x, xi, and xii, along with potentially raised intracranial pressure and other sequelae of jugular venous compression. Collet sicard syndrome, cranial, nerve, carcinoma, metastasis. We describe a rare neurological presentation of internal jugular vein thrombosis induced by central venous catheter placement in a patient with cancer. A 44yearold woman presented with 4 weeks of increasing neck pain and newly arising dysphagia and hoarseness. Colletsicard syndrome as a result of unilateral carotid. Collet sicard syndrome is a rare syndrome that involves paralysis of 9th to 12th cranial nerves. It is associated with various etiologies of tumoral and other origin.
Case report open access colletsicard syndrome as an. Current literature contains only two cases of collet sicard syndrome due to idiopathic internal jugular vein thrombosis. A case of colletsicard syndrome associated with traumatic. It is distinguished from villaret syndrome by lack of presence of sympathetic involvement. On examination, he had left 9th12th cranial neuropathies, manifesting. Colletsicard syndrome from thrombosis of the sigmoid. Collet sicard syndrome is a unique condition involving lesions of the skull base, which affect both the jugular foramen and the hypoglossal canal. The portal can access those files and use them to remember the users data, such as their chosen settings screen view, interface language, etc. Later he became a professor of general pathology in lyon, being appointed professor of. A 71yearold man gave a 3week history of dysphagia and dysarthria with leftsided neck pain and headache. It is associated with various neoplastic and nonneoplastic aetiologies.
Colletsicard syndrome neurologia english edition elsevier. Collet sicard syndrome, carotid artery dissection, cranial nerve palsy. Backgroundcollet sicard syndrome is caused by lesions at the base of the skull affecting the lower cranial nerves. Collet sicard syndrome as an initial presentation of prostate cancer. Colletsicard syndrome associated with occipital condyle. Collet sicard syndrome css is a rarely seen condition characterised by palsies of the lower cranial nerves ix to xii with sparing of the sympathetic plexus. Colletsicard syndrome is caused by lesions at the base of the skull affecting the lower cranial nerves.
This case is unusual because of the diagnosis of bone metastasis secondary to prostate. Pdf the vernet, collet sicard and villaret syndromes are uncommon. Although this syndrome has been reported previously in the literature, most cases are diagnosed as. Colletsicard syndrome css is defined as unilateral palsy of lower cranial nerves ix, x, xi, and xii. Collet sicard syndrome is caused by lesions at the base of the skull affecting the lower cranial nerves. Colletsicard syndrome attributable to extramedullary.
Unilateral paralysis of the last four cranial nerves ixxii is referred to as the collet sicard syndrome. In 1915, frederic collet initially described this syndrome in a soldier who had been shot during world war i, 1 and some time later, jean a. A 56yearold woman presented with headache, vomiting for 3 days, and right hearing loss, tinnitus, and dysphagia over 3 months. The site most frequently affected is the petrous apex, although the external auditory canal, the middle ear and the mastoid apophysis can also be. Collet sicard syndrome refers to unilateral lesions of cranial nerves cn ix, x, xi, and xii. Collet sicard syndrome is a constellation of cranial nerve palsies due to a lesion at the jugular foramen such as a glomus jugulare tumor or schwannoma.
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